Volume 4, Issue 2 (6-2019)                   J Res Dent Maxillofac Sci 2019, 4(2): 37-42 | Back to browse issues page

‎ 10.29252/jrdms.4.2.37

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Developmental Disturbance of Dentin with Probable Diagnosis of Dentin Dysplasia Type 1d: A rare case report
A Rashidian1 , SH Zahraei 2, SS Hashemi3
1- Assistant Professor, Pediatric dentistry Dept, Faculty of Dentistry, Tehran Medical Sciences
2- postgraduate student, Pediatric dentistry Dept, Faculty of Dentistry, Tehran Medical Sciences, Islamic Azad University, Tehran, Iran , shohrehz@gmail.com
3- Post-graduate student, periodontal Dept, faculty of Dentistry,Tehran medical sciences
Abstract:   (2604 Views)

Background: Dentin dysplasia (DD) is a rare disturbance of dentin formation, characterized by normal enamel but atypical dentin formation with abnormal pulpal morphology. In DD type I, the teeth appear clinically normal in morphologic appearance and color. Radiographic analysis shows obliteration of all pulp chambers as well as short, blunted, and malformed or absent roots with multiple periapical radiolucencies involving apparently intact teeth.
Case Presentation: We present a case of a 15-year-old girl with a developmental disturbance of dentin similar to DD type 1. Radiographic examination revealed multiple affected teeth with unique findings in accordance with DD 1d subtype. This article highlights the clinical and radiographic findings of this condition along with the differential diagnosis and management.
Conclusion: Management of patients with DD is difficult and requires a multidisciplinary approach. Early diagnosis of the condition is important for the initiation of effective preventive treatment.

Keywords: Tooth Abnormalities, Dentin Dysplasia, Rootless Teeth
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Type of Study: Case report | Subject: Oral medicin
References
1. 1. de La Dure-Molla M, Philippe Fournier B, Berdal A. Isolated dentinogenesis imperfecta and dentin dysplasia: revision of the classification. Eur J Hum Genet. 2015 Apr;23(4):445-51. [DOI:10.1038/ejhg.2014.159] [PMID] [PMCID]
2. Malik S, Gupta S, Wadhwan V, Suhasini GP. Dentin dysplasia type 1 - A rare entity. J Oral Maxillofac Pathol. 2015 Jan-Apr;19(1):110. [DOI:10.4103/0973-029X.157220] [PMID] [PMCID]
3. Chamberlain BB, Hayward JR. Management of dentin dysplasia and facial disharmony. Spec Care Dentist. 1983 May-Jun;3(3):113-6. [DOI:10.1111/j.1754-4505.1983.tb01615.x] [PMID]
4. Rushton MA. A case of dentin dysplasia. Guys Hosp Rep. 1939;89:369-73.
5. Witkop CJ Jr. Hereditary defects of dentin. Dent Clin North Am. 1975 Jan;19(1):25-45.
6. Fulari SG, Tambake DP. Rootless teeth: Dentin dysplasia type 1. Contemp Clin Dent. 2013 Oct-Dec;4(4):520-522. [DOI:10.4103/0976-237X.123063] [PMID] [PMCID]
7. Daryani D, Nair GR, Naidu G. Dentin dysplasia type II: An exclusive report of two cases in siblings. J Indian Acad Oral Med Radiol. 2017;29:132-4. [DOI:10.4103/jiaomr.JIAOMR_23_16]
8. Sekerci AE, Etoz M, Sahman H, Sisman Y, Nazlim S. A rare condition affecting the primary and permanent dentition: Dentin dysplasia type I. J Oral Maxillofac Radiol. 2013;1(1):13-16. [DOI:10.4103/2321-3841.111346]
9. Xiong F, Ji Z, Liu Y, Zhang Y, Hu L, Yang Q, et al. Mutation in SSUH2 Causes Autosomal-Dominant Dentin Dysplasia Type I. Hum Mutat. 2017 Jan;38(1):95-104. [DOI:10.1002/humu.23130] [PMID]
10. Carmem DVSdM, Lúcia dFAdDM, Heloísa CSS, Markelane SS, Graciela MOS, Marina dDMdL. Dentin Dysplasia Type I-Diagnosis and Treatment: Case Report. Adv Dent & Oral Health. 2017 Oct;6(1):555676. [DOI:10.19080/ADOH.2017.06.555676]
11. Logan J, Becks H, Silverman S Jr, Pinnborg JJ. Dentinal dysplasia. Oral Surg Oral Med Oral Pathol. 1962 Mar;15:317-33. [DOI:10.1016/0030-4220(62)90113-5]
12. Sauk JJ Jr, Lyon HW, Trowbridge HO, Witkop CJ Jr. An electron optic analysis and explanation for the etiology of dentinal dysplasia. Oral Surg Oral Med Oral Pathol. 1972 May;33(5):763-71. [DOI:10.1016/0030-4220(72)90444-6]
13. Wesley RK, Wysocki GP, Mintz SM, Jackson J. Dentin dysplasia type I. Clinical, morphologic, and genetic studies of a case. Oral Surg Oral Med Oral Pathol. 1976 Apr;41(4):516-24. [DOI:10.1016/0030-4220(76)90279-6]
14. Steidler NE, Radden BG, Reade PC. Dentinal dysplasia: A clinicopathological study of eight cases and review of the literature. Br J Oral Maxillofac Surg. 1984 Aug;22(4):274-86. [DOI:10.1016/0266-4356(84)90084-6]
15. O'Carroll MK, Duncan WK, Perkins TM. Dentin dysplasia: review of the literature and a proposed subclassification based on radiographic findings. Oral Surg Oral Med Oral Pathol. 1991 Jul;72(1):119-25. [DOI:10.1016/0030-4220(91)90202-N]
16. Sahoo SR, Aggarwal S. Dentin dysplasia type 1d: A rare case. Indian J Dent Res. 2014 Nov-Dec;25(6):832-4. [DOI:10.4103/0970-9290.152217] [PMID]
17. American Academy of Pediatric Dentistry. Guideline on dental management of heritable dental developmental anomalies. Pediatr Dent. 2013 Sep-Oct;35(5):E179-84.
18. Khandelwal S, Gupta D, Likhyani L. A Case of Dentin Dysplasia with Full Mouth Rehabilitation: A 3-year Longitudinal Study. Int J Clin Pediatr Dent. 2014 May-Aug;7(2):119-124. [DOI:10.5005/jp-journals-10005-1248] [PMID] [PMCID]
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